Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

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This report describes two cases of hypertrophic cranial pachymeningitis and briefly discusses the clinical and radiographic, findings.

Neurological complications of sarcoidosis. The relationship of idiopathic hypertrophic pachymeningitis with connective tissue disease or vasculitis syndrome is discussed.

This is an open-access article distributed under the terms of the Creative Pavhymeningitis Attribution-Noncommercial-Share Alike 3.

The clinical course was chronic. A case of chronic hypertrophic cranial pachymeningitis causing cranial polyneuropathy and unilateral central retinal vein occlusion. Eur J Radiol ; Idiopathic hypertrophic cranial pachymeningitis with perifocal brain edema.


Hypertrophic pachymeningitis

Axial section pachymeninbitis MRI image showing diffuse enhacement with thickening of meninges. The cell infiltration was marked at the surface of the dura mater.

CT or MR imaging studies should be obtained to identify mass lesions in the brain stem or skull base. Cranial pachymeningitis typically cause progressive cranial nerve palsies, headaches, and cerebellar dysfunction. Pathological examination in two autopsied cases pahymeningitis diffuse thickening of the dura, especially in the posterior part of the falx cerebri and the tentorium cerebelli.

Combined therapy of corticosteroid and azathioprine in hypertrophic cranial pachymeningitis. Neurology and general medicine.

Presence of associated leptomeningeal enhancement or parenchymal abnormalities with the exception of brain edema should suggest an alternate diagnosis. About Blog Go ad-free. N Engl J Med; The CSF in most cases showed inflammatory changes. A year-old male came to ER with headache associated with vomiting since 2 weeks and pachyeningitis episode of right focal seizure.

Idiopathic hypertrophic pachymeningitis.

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Pardee I, Knox lC: To quiz yourself on this article, log in to see multiple choice questions. Idiopathic hypertrophic cranial pachymeningitis. Loading Stack – 0 images remaining. No To Shinkei ; Idiopathic hypertrophic chronic pachymeningitis presenting with acute visual loss.


Click on image for details. Support Center Support Center. Neurol Med Chir ; It can involve the cranial or the spinal dura or both. Neuroimaging studies revealed diffuse or localized thickening of the dura, pachymenningitis MRI findings were key to diagnosis of this disorder.

Hypertrophic pachymeningitis

Herein are described pachymdningitis patients with idiopathic hypertrophic pachymeningitis; their clinical, laboratory and radiological findings, as well as their treatment, are analyzed. Neuropathological findings of six cases including two autopsied cases are also presented.

It was pachymwningitis described by Charcot and later by Naffziger and Stern. This article has been cited by other articles in PMC. Eur Neurol ; BhanuSakthi Velayuthamand M.