The full Klüver-Bucy syndrome (KBS) – hyperorality, placidity, hypermetamorphosis, dietary changes, altered sexual behavior, and visual. Klüver-Bucy syndrome is a very rare cerebral neurological disorder associated with damage to both temporal lobes resulting in abnormalities in memory, social . Klüver-Bucy syndrome is described here because its cause is usually bilateral lesions in the territory of the PCAs. In the small number of reports of the syndrome .

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Major symptoms may include excessive oral tendencies with an urge to put all kinds of objects into kluvet mouth, hypermetamorophosis a need to explore everythingmemory loss, emotional changes, extreme sexual behavior, indifference, placidity, visual distractibility and visual agnosia difficulty identifying and processing visual information.

Disorders typically diagnosed in childhood. Frontotemporal degeneration is a very rare progressive neurological disease initially predominately affecting the frontal and temporal lobes of the brain. All studies receiving U. Government funding, and some supported by private industry, are posted on this government web site. D ICD – KBS is now thought to be caused by disturbances of temporal portions of limbic networks that interface with multiple cortical and subcortical circuits to modulate emotional behavior and affect.

From Wikipedia, the free encyclopedia. Some KBS features i. Goscinski I, et al. X-linked intellectual disability Lujan—Fryns syndrome. Bergman; Ronald Arly Bergman Human KBS does not occur in isolation, but is typically part of a complex behavioral syndrome that almost always includes amnesia and aphasia, and that may also include dementia and seizures. Personality disorder Impulse control disorder Kleptomania Trichotillomania Pyromania Dermatillomania Factitious disorder Munchausen syndrome.


Sexual maturation disorder Ego-dystonic sexual orientation Sexual relationship disorder Paraphilia Voyeurism Fetishism. Comparisons may be useful for a differential diagnosis: First aired June 27, What Neuroscience Reveals about Morality. Bilateral ventral temporal ablations and bilateral temporal lobectomies produced marked impairment in visual discrimination, whereas lateral resections or unilateral lesions did not.

Klüver-Bucy Syndrome – NORD (National Organization for Rare Disorders)

Adjustment disorder with depressed mood. The content of the website and databases of the National Organization for Rare Disorders NORD is copyrighted and may not be reproduced, copied, downloaded or disseminated, in any way, for any commercial or public purpose, without prior written authorization and approval from NORD.

Social neurosciences research shows that changes in temporal lobe is identified as a cause for aberrant sexual and hyper-sexual behaviors. There may also be other symptoms associated with dementia loss of reason as well. Delirium Post-concussion syndrome Organic brain syndrome. Retrieved from ” https: Hayman LA, et al.

Views Read Edit View history. Schizoaffective disorder Schizophreniform disorder Brief reactive psychosis. The Kluver-Bucy syndrome is a clinical syndrome observed in humans and other animals after bilateral lesions in the temporal lobe that involve sgndrome amygdala, hippocampal formation, and adjacent neural structures.

Human cases were recognized in the s, as surgeons employed bilateral temporal lobectomies to treat seizures. For information about clinical trials sponsored by private sources, contact: As memory losses increase, personality, mood and behavior also tend to change.

Kluger of Neurology, 6th ed.

Rare Disease Database

Alone we are rare. Disorganized hebephrenic schizophrenia Paranoid schizophrenia Simple-type schizophrenia Childhood schizophrenia Pseudoneurotic schizophrenia.

An almost uncontrollable appetite for food may also be noted. Dissociative identity disorder Psychogenic amnesia Fugue state Depersonalization disorder. First aired September 12, Psychoactive substances, substance abuse and substance-related disorders. It is characterized by progressive deterioration of intellect with changes in behavior and personality. About News Events Contact. The treatment of KBS is difficult and often unsatisfactory.


Disorders typically diagnosed in childhood Intellectual disability X-linked intellectual disability Lujan—Fryns syndrome. Postpartum depression Postpartum psychosis. Alzheimer disease is a common progressive disorder of the brain affecting memory, thought and language.

Box Bethesda, MD Phone: Various attempts were made to localize the component features to specific areas of the temporal lobe, with mixed success.

Comparisons may be useful for a differential diagnosis:. Schizophreniaschizotypal and delusional. Some current clinical trials also are posted on the following page on the NORD website: Adult personality and behavior Gender dysphoria Sexual maturation disorder Ego-dystonic sexual orientation Sexual relationship disorder Paraphilia Voyeurism Fetishism.

However, in later stages there is loss of motor control as well as confusion and severe dementia.

Kluver-Bucy Syndrome – Temporal Lobectomy Behavior Syndrome – information page with HONselect

Iluver, concentration, speech and physical coordination may also be affected. Investigational Therapies Information on current clinical trials is posted on the Internet at www. Information on current clinical trials is posted on the Internet at www. Infobox medical condition new.